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Indian Journal of Cancer
Medknow Publications on behalf of Indian Cancer Society
ISSN: 0019-509X EISSN: 0019-509X
Vol. 45, No. 2, 2008, pp. 64-66
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Bioline Code: cn08017
Full paper language: English
Document type: Case Report
Document available free of charge
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Indian Journal of Cancer, Vol. 45, No. 2, 2008, pp. 64-66
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Wunderlich's syndrome with hepatic angiomyolipoma in tuberous sclerosis
Mongha R; Bansal P; Dutta A; Das RK & Kundu AK
Abstract
We present a patient of tuberous sclerosis complex with bilateral renal angiomyolipoma and hepatic angiomyolipoma with spontaneous retroperitoneal hemorrhage from right angiomyolipoma (Wunderlich′s syndrome). Nephron preserving approach was tried but the right kidney could not be salvaged. Hepatic angiomyolipoma was managed conservatively. Wunderlich′s syndrome has been found in around 10% of cases of renal angiomyolipomas. Hepatic Angiomyolipoma is a benign mesenchymal neoplasm of the liver which is rarely reported in literature
Keywords
Angiomyolipoma, hepatic, renal, tuberous sclerosis
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© Copyright 2008 Indian Journal of Cancer. Alternative site location: http://www.indianjcancer.com/
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