Indian Journal of Surgery
Medknow Publications on behalf of Association of Surgeons of India
Vol. 68, No. 6, 2006, pp. 320-321
Bioline Code: is06093
Full paper language: English
Document type: Research Article
Document available free of charge
Indian Journal of Surgery, Vol. 68, No. 6, 2006, pp. 320-321
© Copyright 2006 Indian Journal of Surgery.
Case Report-Mega-duodenum due to isolated segmental duodenal aganglionosis|
Barmeda ShaileshH, Porecha MehulM, Bhimbhara PanchampalS, Mehta PurviJ, Vasavada HiralD, Sharma NirajJ
Isolated segmental duodenal aganglionosis is an extremely rare condition. We report a case of mega-duodenum due to an isolated aganglionic segment in the second part of the duodenum. A 60-year-old female presented with a history of off-and-on non-bilious vomiting and upper abdominal fullness after each meal. Investigations suggested that the stomach and the first part of the duodenum were grossly dilated. On exploration, a narrowed segment in the second part of the duodenum with gross dilation of the proximal duodenum and the stomach was found. Retrocolic duodenojejunostomy was done and a biopsy was taken from the narrowed duodenal segment. Histopathology examination revealed near-complete absence of the ganglion cells in the narrowed segment.
Aganglionosis, double bubble appearance, duodenojejunostomy, mega-duodenum