search
for
 About Bioline  All Journals  Testimonials  Membership  News  Donations


Neurology India
Medknow Publications on behalf of the Neurological Society of India
ISSN: 0028-3886
EISSN: 1998-4022
Vol. 55, No. 4, 2007, pp. 413-415
Bioline Code: ni07122
Full paper language: English
Document type: Case Report
Document available free of charge

Neurology India, Vol. 55, No. 4, 2007, pp. 413-415

 en Case Report - Acute intermittent porphyria presenting with neurological emergency: Review of six cases
Kochar, Dhanpat K; Pal, Mahender; Kochar, Sanjay Kumar; Vyas, Arvind; Kochar, Abhishek; Bindal, Dinesh & Agrawal, Rajender Prasad

Abstract

Acute intermittent porphyria presenting with short duration of gastrointestinal symptoms followed by rapidly progressive fulminant neurological syndrome during first attack is relatively uncommon. It is a neurological emergency and mimics many other psychiatric and medical disorders and can be fatal if it remains undiagnosed and untreated. Further, specific treatment in the form of Heme arginate is not universally available and very costly, so high clinical suspicion and early diagnosis and management of acute attack and prevention of further attacks are very important. We report a series of six cases who presented with convulsion and/or polyneuropathy early in the course of disease to highlight this fact.

Keywords
Acute intermittent porphyria, convulsion, neurological emergency

 
© Copyright 2007 Neurology India.
Alternative site location: http://www.neurologyindia.com

Home Faq Resources Email Bioline
© Bioline International, 1989 - 2019, Site last up-dated on 30-Oct-2019.
Site created and maintained by the Reference Center on Environmental Information, CRIA, Brazil
System hosted by the Internet Data Center of Rede Nacional de Ensino e Pesquisa, RNP, Brazil