Iranian Journal of Pediatrics
Tehran University of Medical Sciences Press
Vol. 18, No. 1, 2008, pp. 62-66
Bioline Code: pe08010
Full paper language: English
Document type: Case Report
Document available free of charge
Iranian Journal of Pediatrics, Vol. 18, No. 1, 2008, pp. 62-66
© Copyright 2008 - TUMS PUBLICATIONS
Congenital Embryonal Rhabdomyosarcoma with Prenatal Onset|
Khatami, Fatemeh; Bazrafshan, Ahmad; Monajemzadeh, Maryam & Seyed, Masood
Rhabdomyosarcoma (RMS) is the single most common type of soft tissue sarcoma in children and adolescents but it is extraordinarily rare in neonates. Extremity RMS comprises 20% of all sites, occurs more commonly in the leg than in the arm and accounts for 9% of all RMS cases.
Case Presentation:According to our review, this is the second case of RMS on day one of life with congenital, antenatal feature, and postnatal progressive clinical course of a large tumor of the hand (pre‐treatment staging T2bN1M0) with embryonic histological subtype and unfavorable prognosis. The patient is a term newborn boy with huge mass in the right hand and palpable lymph node in subaxillar region.
Congenital embryonal rhabdomyosarcoma is a rare form of sarcomas with congenital in nature, .antenatal feature and post natal progressive clinical course of sarcomas of extremities in newborn infants.
Congenital, Rhabdomyosarcoma, Embryonal, Antenatal
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