Iranian Journal of Pediatrics
Tehran University of Medical Sciences Press
Vol. 25, No. 5, 2015, pp. 1-4
Bioline Code: pe15072
Full paper language: English
Document type: Case Report
Document available free of charge
Iranian Journal of Pediatrics, Vol. 25, No. 5, 2015, pp. 1-4
© Copyright 2015 - Iranian Journal of Pediatrics
Persistent Truncus Arteriosus With Intact Ventricular Septum: Clinical, Hemodynamic and Short-term Surgical Outcome|
Ajami, Gholamhossein; Amirghofran, Ahmad Ali; Amoozgar, Hamid & Borzouee, Mohammad
Introduction: Truncus arteriosus with intact ventricular septum is a rare and unique variant of persistent truncus arteriosus (PTA) which usually presents with central cyanosis and congestive heart failure in neonate and early infancy. Associated cardiac and non-cardiac anomalies may affect morbidity and mortality of these patients.
Case Presentation: We describe clinical presentation, echocardiography and angiographic features of a 7-month old boy with PTA and intact ventricular septum who underwent surgical repair of the anomaly at our institution. Operative findings, surgical procedure and short-term outcome are reported.
Conclusions: While our patient had systemic pulmonary arterial pressure at the time of complete surgical repair, it was improved after surgery.
Truncus Arteriosus; Persistent; Intact Ventricular Septum; Outcome
Alternative site location: http://diglib.tums.ac.ir/pub/