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Iranian Journal of Pediatrics
Tehran University of Medical Sciences Press
ISSN: 1018-4406
EISSN: 2008-2150
Vol. 26, No. 5, 2016, pp. 111-112
Bioline Code: pe16081
Full paper language: English
Document type: Case Report
Document available free of charge

Iranian Journal of Pediatrics, Vol. 26, No. 5, 2016, pp. 111-112

 en Anesthetic Management in a Child With Niemann-Pick Disease
Espahbodi, Ebrahim; Yaghooti, Amir Abbas; Ostadalipour, Abbas & Marashi, Shaqayeq

Abstract

Niemann-Pick is a lipid storage disease that results from a lysosomal enzyme deficiency (sphingomyelinase). It has different presentations, and it may affect various organs such as the central nervous system, kidney, liver, and spleen. Due to the complexity of the disease, careful perianesthetic management is necessary in order to reduce the risks and sequels. As there is little evidence available in the literature regarding the anesthetic implications of such patients, in this case report we describe the anesthetic management of a two-year-old female with Niemann-Pick disease.

Keywords
Niemann-Pick; Anesthesia; Child

 
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