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International Journal of Reproductive BioMedicine
Research and Clinical Center for Infertility, Shahid Sadoughi University of Medical Sciences of Yazd
ISSN: 1680-6433 EISSN: 1680-6433
Vol. 17, No. 11, 2019, pp. 851-856
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Bioline Code: rm19088
Full paper language: English
Document type: Case Report
Document available free of charge
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International Journal of Reproductive BioMedicine, Vol. 17, No. 11, 2019, pp. 851-856
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An unusual appearance of the post-pubertal Herlyn-Werner-Wunderlich syndrome with acute abdominal pain: A case report
Ghasemi, Marzieh & Esmailzadeh, Arezoo
Abstract
Background: Herlyn-Werner-Wunderlich (HWW) syndrome is a rare congenital urogenital
defect. It is detected by unilateral low vaginal obstruction, uterus didelphys, and
ipsilateral kidney agenesis. It usually becomes apparent with pain, dysmenorrhea, and
presence of a vaginal or pelvic mass. Purulent vaginal discharge may also happen
rarely because of infective complications of the obstructed hemivagina. In this report,
we describe a post-pubertal case with acute abdominal pain.
Case: The patient was a 13-yr-old girl who was referred to us with acute abdominal
pain one year after the onset of her menarche. In the pelvic examination, we detected
hematocolpos. Abdominopelvic-computed tomography scan confirmed the presence
of mullerian duct anomalies with uterus didelphys. This case of HWW syndrome along
with pyocolpus was managed by vaginal septum resection, drainage of pus, and
salpingectomy.
Conclusion: The symptoms of HWW syndrome should be monitored in early puberty
to prevent more complications.
Keywords
Herlyn-Werner-Wunderlich syndrome; Uterus didelphys; Kidney agenesis; Mullerian duct anomaly.
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© Copyright 2019 - Marzieh Ghasemi and Arezoo Esmailzadeh Alternative site location: http://www.ijrm.ir
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